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Case Reports
. 2015 Jul-Sep;10(3):237-9.
doi: 10.4103/1817-1745.165665.

Diastematomyelia with hemimyelomeningocele: An exceptional and complex spinal dysraphism

Neha Singh  1 , Deepak Kumar Singh  2 , Rakesh Kumar  2
Affiliations
Case Reports

Diastematomyelia with hemimyelomeningocele: An exceptional and complex spinal dysraphism

Neha Singh et al. J Pediatr Neurosci. 2015 Jul-Sep.

Abstract

Variations in split cord malformation (SCM) have been described earlier. However, a true hemimyelomeningocele (HMM) as only congenital malformation is extremely rare and is reported infrequently in published literature. We are reporting the case of a 3-month-old girl child who presented with a swelling on the lower back since birth. Magnetic resonance imaging revealed a type 1 SCM with right hemicord forming a HMM. Precise diagnosis and thorough anatomical detail of dysraphism is essential for optimal, individualized neurosurgical management.

Keywords: Diastematomyelia; hemimyelomeningocele; spinal dysraphism; split cord malformation type 1.

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Figures

Figure 1
Figure 1
T2-weighted sagittal (a) and coronal (b) magnetic resonance imaging of dorso-lumbar spine shows a hemivertebrae from D10 to D12 level along with a bony spur at D11. Tethering of cord and meningomyelocele is also visible. Continuation of left hemicord is appreciable in coronal view (b)
Figure 2
Figure 2
T2 weighted axial image shows a bony spur dividing the cord into two halves (a and b). Herniation of right hemicord, meninges and cerebrospinal fluid is noted through the defect in posterior element, forming a large hemi-meningomyelocele (c). Two hemicords are visible below the level of herniation (d) which reunites at D12 level to form a single cord (e)
See this image and copyright information in PMC

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