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. 2015:2015:581394.
doi: 10.1155/2015/581394. Epub 2015 Oct 26.

Klippel-Trenaunay Syndrome with Extensive Lymphangiomas

Sirin Mneimneh  1 , Ali Tabaja  1 , Mariam Rajab  1
Affiliations

Klippel-Trenaunay Syndrome with Extensive Lymphangiomas

Sirin Mneimneh et al. Case Rep Pediatr. 2015.

Abstract

Klippel-Trenaunay syndrome (KTS) is a rare disorder characterized by the triad of vascular malformations, venous varicosities, and bone and soft-tissue hypertrophy. We present a case of Klippel-Trenaunay syndrome with limb hypertrophy, port-wine stains, lymphangiomas, and venous varicosities in the limbs.

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Figures

Figure 1
Figure 1
Focal overgrowth over the upper part of the chest.
Figure 2
Figure 2
Multiple focal overgrowth of the right arm.
Figure 3
Figure 3
Port-wine stain over the back and thigh.
Figure 4
Figure 4
Hypertrophy of the left thigh.
Figure 5
Figure 5
Syndactyly of the toes in both feet.
Figure 6
Figure 6
X-ray. (a) Right foot; (b) left foot.
Figure 7
Figure 7
MRI of the chest (phase T2 sequence, with fat suppression), showed the lymphangioma in the upper part of the chest wall, in the right arm.
Figure 8
Figure 8
MRI of the abdomen showed the hemangioma in the spleen.
See this image and copyright information in PMC

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