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. 2015:2015:419408.
doi: 10.1155/2015/419408. Epub 2015 Nov 25.

Susac's Syndrome: A Case with Unusual Cardiac Vestibular and Imaging Manifestations

Yaron River  1 , Avi Shupak  2 , Beatrice Tiosano  3 , Vika Danilov  1 , Itzhak Braverman  4
Affiliations

Susac's Syndrome: A Case with Unusual Cardiac Vestibular and Imaging Manifestations

Yaron River et al. Case Rep Neurol Med. 2015.

Abstract

Susac's syndrome (SS) is a disease of the microvasculature of the retina, brain, and inner ear. We describe a patient with unusual manifestations of SS with possible involvement of the brainstem, cardiac arrhythmia, and MRI findings lacking the characteristic lesions found in Susac's syndrome.

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Figures

Figure 1
Figure 1
EKG: note the bradycardia and inverted P waves (II; III; AVF) 6 days following admission.
Figure 2
Figure 2
Left panel: ocular coherence tomography. Note the widening of the inner retinal layer signifying retinal edema three weeks following admission. Right panel: right eye visual field. Note the central scotoma.
Figure 3
Figure 3
MRI-FLAIR protocol. Left: initial MRI, 04/12. Right: MRI following relapse 10/12. Note a diffuse hyperintense, ill-defined, left hemispheric centrum semiovale lesion superior to the lateral ventricles (black arrow).
See this image and copyright information in PMC

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