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Case Reports
. 2016 Jan 19:2016:bcr2015212387.
doi: 10.1136/bcr-2015-212387.

An atypical case of dermatomyositis associated with chromophobe renal cell carcinoma

Michael David George  1 , Arash H Lahouti  2 , Lisa Christopher-Stine  2
Affiliations
Case Reports

An atypical case of dermatomyositis associated with chromophobe renal cell carcinoma

Michael David George et al. BMJ Case Rep. .

Abstract

Dermatomyositis and polymyositis are the major idiopathic inflammatory myopathies in adults. They are associated with an elevated risk of malignancy. However, renal tumours have rarely been described in dermatomyositis patients. We report the case of a 27-year-old Caucasian man with chromophobe renal cell cancer (ChRCC) and antinuclear matrix protein (NXP-2)-associated dermatomyositis. To the best of our knowledge, there are no previous reports of ChRCC presenting with dermatomyositis.

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Figures

Figure 1
Figure 1
Coronal short τ inversion recovery MRI showing extensive oedema in thigh muscles.
Figure 2
Figure 2
H&E staining showing smaller muscle fibres at the periphery of the fascicles (perifascicular atrophy).
See this image and copyright information in PMC

References

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