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Case Reports
. 2016 Jan-Mar;6(1):57-9.
doi: 10.4103/2229-516X.174016.

Dyke-Davidoff-Masson syndrome

N Vinay Kumar  1 , T S Gugapriya  1 , Arun T Guru  2 , Sd Nalina Kumari  1
Affiliations
Case Reports

Dyke-Davidoff-Masson syndrome

N Vinay Kumar et al. Int J Appl Basic Med Res. 2016 Jan-Mar.

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) refers to atrophy or hypoplasia of one cerebral hemisphere, due to an insult to the developing brain in fetal or early childhood period. Age of presentation depends on the time of neurologic insult, and characteristic changes may be seen only in adolescence. Male gender and left hemisphere are more frequently involved. A 17-year-old female adolescent with a history of recurrent refractory seizures, hemiplegia and mental retardation reported to Department of Radiology for computed tomography (CT) assessment of brain. On examination, she had facial asymmetry, delayed milestones, and spastic hemiplegia. The CT brain showed right cortical atrophy with ventricular dilatation, prominent sulci, and shifting of falx to the right side. Bone window image showed asymmetry in skull vault thickness, the width of diploic space, the size of paranasal air sinuses and inclination of the petrous ridge between the affected and normal sides. As the above case deviates from the usual presentation of male left sided DDMS, hence the report.

Keywords: Cerebral atrophy; paranasal air sinuses; petrous ridge; prominent sulci.

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Figures

Figure 1
Figure 1
Right cerebral hemiatrophy (CH) with prominent sulci, lateral ventricular dilatation (LVD), falx displacement (FD)
Figure 2
Figure 2
Thick skull vault with widened diploic space (SD)
Figure 3
Figure 3
Elevated petrous ridge (EP) and larger mastoid air cells (M)
See this image and copyright information in PMC

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