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Review
. 2016 Mar;18(3):240-6.
doi: 10.1111/jch.12650. Epub 2015 Aug 19.

Renal Fibromuscular Dysplasia: A Not So Common Entity of Secondary Hypertension

Elias A Sanidas  1 , Maria Seferou  1 , Dimitris P Papadopoulos  1 , Anastasios Makris  1 , Nora A Viniou  1 , Vasiliki Chantziara  1 , Vasiliki Cennimata  1 , Vasilios Papademetriou  2
Affiliations
Review

Renal Fibromuscular Dysplasia: A Not So Common Entity of Secondary Hypertension

Elias A Sanidas et al. J Clin Hypertens (Greenwich). 2016 Mar.

Abstract

Fibromuscular dysplasia is a rare noninflammatory vascular disease characterized by nonatheroslerotic stenosis predominantly seen in young women, whereas the majority of cases involve the renal arteries causing secondary hypertension. Most noninvasive screening tests are not quite sensitive or reproducible to rule out renal artery stenosis, but renal angiography usually confirms the diagnosis. Percutaneous renal artery angioplasty is the treatment of choice; however, it may not result in normalization of blood pressure if diagnosis is delayed. Continued follow-up is necessary since stenosis reoccurs.

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Figures

Figure 1
Figure 1
Baseline preintervention angiography of the right renal artery showing the typical “string‐of‐beads” morphology illusive for the diagnosis of fibromuscular dysplasia.
Figure 2
Figure 2
Postintervention angiography of the right renal artery without the typical “string‐of‐beads” morphology of fibromuscular dysplasia. PCI indicates percutaneous coronary intervention.
See this image and copyright information in PMC

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