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. 2016:2016:1484089.
doi: 10.1155/2016/1484089. Epub 2016 Feb 14.

Glucagonoma and Glucagonoma Syndrome: A Case Report with Review of Recent Advances in Management

Ashraf Al-Faouri  1 , Khaled Ajarma  1 , Samer Alghazawi  1 , Sura Al-Rawabdeh  2 , Adnan Zayadeen  3
Affiliations

Glucagonoma and Glucagonoma Syndrome: A Case Report with Review of Recent Advances in Management

Ashraf Al-Faouri et al. Case Rep Surg. 2016.

Abstract

The rarity of glucagonoma imposes a challenge with most patients being diagnosed after a long period of treatment for their skin rash (months-years). Awareness of physicians and dermatologists of the characteristic necrolytic migratory erythema often leads to early diagnosis. Early diagnosis of glucagonoma even in the presence of resectable liver metastases may allow curative resection. Herein, we present a typical case of glucagonoma treated at our center and review the literature pertinent to its management.

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Figures

Figure 1
Figure 1
Necrolytic migratory erythema over the back with areas of healing and hyperpigmentation.
Figure 2
Figure 2
Glossitis.
Figure 3
Figure 3
Onychoschizia.
Figure 4
Figure 4
Hypervascular tumor in the tail of pancreas with metastases in segment V of the liver.
Figure 5
Figure 5
Glucagonoma in the tail of pancreas.
See this image and copyright information in PMC

References

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