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Case Reports
. 2016 Apr;21(2):164-7.
doi: 10.17712/nsj.2016.2.20150164.

Acquired hepatocerebral degeneration

Destina Yalcin  1 , Emel Oguz-Akarsu, Mehmet Sokmen
Affiliations
Case Reports

Acquired hepatocerebral degeneration

Destina Yalcin et al. Neurosciences (Riyadh). 2016 Apr.

Abstract

Acquired hepatocerebral degeneration is a rare, mostly irreversible neurological syndrome that occurs in patients with chronic liver disease, particularly in those with surgically or spontaneously induced portosystemic shunts. Typical magnetic resonance findings are T1 hyperintensity in the pallidum, substantia nigra, periaquaductal gray matter. In this paper, we report a case of a 51-year-old woman presented with hepatic encephalopathy episodes and typical magnetic resonance findings, who does not develop any neurological signs or symptoms, nor cognitive decline in the follow up period, lasting for 3 years.

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Figures

Figure 1
Figure 1
The electroencephalography during the confusion attack showing triphasic waves.
Figure 2
Figure 2
T1-weighted axial magnetic resonance image shows bilateral symmetrical abnormal hyperintensity in the substantia nigra.
Figure 3
Figure 3
T1-weighted axial magnetic resonance image shows bilateral symmetrical abnormal hyperintensity in the globus pallidus.
Figure 4
Figure 4
The electroencephalography recorded one day after the episode showed slow waves in theta range (7-7,5 cys/sec) but no triphasic waves.
See this image and copyright information in PMC

References

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