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Case Reports
. 2016 Mar 16;4(4):429-31.
doi: 10.1002/ccr3.525. eCollection 2016 Apr.

Severe cerebral involvement due to idiopathic systemic capillary leak syndrome

Ali Riza Günes  1 , Peter Berlit  1 , Ralph Weber  1
Affiliations
Case Reports

Severe cerebral involvement due to idiopathic systemic capillary leak syndrome

Ali Riza Günes et al. Clin Case Rep. .

Abstract

The idiopathic systemic capillary leak syndrome (ISCLS) is a rare disorder, characterized by recurrent attacks of hypotension, hypoalbuminemia, and hemoconcentration, which is often misdiagnosed due to overlapping features with other diseases. Even though cerebral involvement is uncommon, a broad awareness is crucial, because of its life-threatening character.

Keywords: coma; critical care; neurology; systemic disease.

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Figure 1
Serial contrast‐enhanced (A + B) and T2‐weighted (C‐F) MRI.
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