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Case Reports
. 2016 Mar;10(3):QD09-11.
doi: 10.7860/JCDR/2016/18516.7513. Epub 2016 Mar 1.

An Unusual Origin of Fetal Lymphangioma Filling Right Axilla

Ali Ozgur Ersoy  1 , Efser Oztas  1 , Erdinc Saridogan  1 , Sibel Ozler  1 , Nuri Danisman  1
Affiliations
Case Reports

An Unusual Origin of Fetal Lymphangioma Filling Right Axilla

Ali Ozgur Ersoy et al. J Clin Diagn Res. 2016 Mar.

Abstract

Fetal lymphangioma is a hamartomatous congenital anomaly of the lymphatic system, which is embracing the fetal skin (sometimes mucous membranes) and the subcutaneous tissue. The general consensus is that it occurs as a result of failure in lymphatic drainage. A 36-year-old pregnant woman was referred to our perinatology clinic at 22 weeks' gestation, because of a fetal right-sided axillary mass revealed by ultrasonography. The mass measuring 5x7x7cm in three dimensions had a multilocular structure without colour Doppler flow and well-circumscribed borders. Amniocentesis revealed a normal constitutional karyotyping. Lymphangioma was considered as prediagnosis. A healthy female baby weighing 3470 grams was delivered at term. Neonatal examination and the postnatal MRI confirmed the diagnosis. The baby is still on follow-up with the medical treatment of Sirolimus an anti-proliferative drug, and the mass got smaller significantly in 8 months after delivery.

Keywords: Axillary mass; Chest wall mass; Karyotyping; Magnetic resonance imaging.

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Figures

[Table/Fig-1]:
[Table/Fig-1]:
Ultrasonographic view of the multilocular cystic mass filling the right fetal axilla.
[Table/Fig-2]:
[Table/Fig-2]:
Postnatal view of the mass and minor skin discolourations on the ipsilateral upper extremity.
[Table/Fig-3]:
[Table/Fig-3]:
T2-weighted magnetic resonance imaging of the mass and intense enhancement of the contrast material by the cyst walls and septa.
[Table/Fig-4]:
[Table/Fig-4]:
The tension of the mass was eased, the covering skin loosened and folded significantly, in an 8 months of continuous treatment with Sirolimus.
See this image and copyright information in PMC

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