An Aggressive Retroperitoneal Fibromatosis

Abstract

Introduction: Aggressive fibromatosis (AF) is a heterogeneous group of mesenchymal tumors that have locally infiltrative growth and a tendency to relapse. The clinical picture is often conditioned by the obstruction of the ureter or small intestine. Diagnosis is based on clinical, radiological and histological parameters.

A case report: We report a case of male patient, aged 35 years, with the retroperitoneal fibromatosis. He reported to the physician because of frequent urination with the feeling of pressure and pain. Computed tomography revealed the tumor mass on the front wall of the bladder with diameter of 70mm with signs of infiltration of the musculature of the anterior abdominal wall. Endoscopic transurethral biopsy showed proliferative lesion binders by type of fibromatosis. The tumor was surgically removed in a classical way. The patient feels well and has no recurrence thirty-six months after the operative procedure.

Conclusion: The complete tumor resection is the therapeutic choice for the primary tumor as well as for a relapse.

Keywords: aggressive fibromatosis; desmoid; radiation therapy; relapse; surgery.

Figure 1

CT - tumor mass of the front wall of the urinary bladder

Figure 2

CT - tumor mass on the front wall of the urinary bladder

Figure 3

CT - infiltration of the musculature of the anterior abdominal wall

Figrue 4

MRI of the abdomen and pelvis - no signs of recurence of the underlying disease