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Case Reports
. 2016 Apr;91(2):240-2.
doi: 10.1590/abd1806-4841.20164300.

Isolated plexiform neurofibroma mimicking a vascular lesion

Paola Cecilia Stefano  1 , Sebastian Nicolas Apa  1 , Agustina Maria Lanoël  1 , Josefina Sala María  1 , Sergio Sierre  1 , Adrián Martin Pierini  1
Affiliations
Case Reports

Isolated plexiform neurofibroma mimicking a vascular lesion

Paola Cecilia Stefano et al. An Bras Dermatol. 2016 Apr.

Abstract

Plexiform neurofibromas are benign tumors originating from peripheral nerve sheaths, generally associated with Neurofibromatosis Type 1 (NF1). They are diffuse, painful and sometimes locally invasive, generating cosmetic problems. This report discusses an adolescent patient who presented with an isolated, giant plexiform neurofibroma on her leg that was confused with a vascular lesion due to its clinical aspects. Once the diagnosis was confirmed by surgical biopsy, excision of the lesion was performed with improvement of the symptoms.

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Conflict of interest statement

Conflict of Interest: None.

Figures

Figure 1
Figure 1
Tumor with hyperpigmented and circular areas
Figure 2
Figure 2
Conglomerate mass in the MRI, hypointense on T1 and low endovenous contrast enhancement
Figure 3
Figure 3
Intraoperative image
Figure 4
Figure 4
H and E 40x. Fusiform cell proliferation disposed into nodules
Figure 5
Figure 5
H and E 400x. Fusiform cell proliferation. Nuclei in italic S
See this image and copyright information in PMC

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