Case Reports
doi: 10.1001/archpedi.1978.02120280025005.
Nocturnal intragastric infusion of glucose in management of defective gluconeogenesis with hypoglycemia
- PMID: 272848
- DOI: 10.1001/archpedi.1978.02120280025005
Item in Clipboard
Case Reports
Nocturnal intragastric infusion of glucose in management of defective gluconeogenesis with hypoglycemia
Am J Dis Child.
1978 Mar.
Abstract
Three children with defective gluconeogenesis and hypoglycemia were treated with frequent daytime feeding and continuous intragastric infusion of glucose at night. By this technique, the blood glucose level was maintained at or slightly above the physiological range. Secondary lacticacidemia, hyperlipidemia, hyperuricacidemia, and coagulation defects all improved. Weight and height velocity increased dramatically. Strength and sense of well-being improved. Nocturnal intragastric infusion of glucose is now the management of choice for children with defective gluconeogenesis and hypoglycemia.
Similar articles
-
Efficacy of cornstarch therapy in type III glycogen-storage disease.Am J Clin Nutr. 1990 Oct;52(4):671-4. doi: 10.1093/ajcn/52.4.671. Am J Clin Nutr. 1990. PMID: 2403059
-
Intragastric feeding in type I glycogen storage disease: factors affecting the control of lactic acidemia.Pediatr Res. 1981 Dec;15(12):1504-8. doi: 10.1203/00006450-198112000-00010. Pediatr Res. 1981. PMID: 6798537
-
[Continuous nocturnal intragastric feeding in glycogenosis type I and III].Pediatrie. 1986 Apr-May;41(3):197-203. Pediatrie. 1986. PMID: 3095784 French.
-
Hypoglycemia in infants and children.Endocrinol Metab Clin North Am. 1999 Sep;28(3):619-46, vii. doi: 10.1016/s0889-8529(05)70091-8. Endocrinol Metab Clin North Am. 1999. PMID: 10500934 Review.
-
[Rare causes of hypoglycemia in adults--glycogen storage diseases].Pol Merkur Lekarski. 2011 Feb;30(176):143-6. Pol Merkur Lekarski. 2011. PMID: 21544986 Review. Polish.
Cited by
-
Effects of cornstarch treatment in very young children with type I glycogen storage disease.Eur J Pediatr. 1990 Jun;149(9):630-3. doi: 10.1007/BF02034750. Eur J Pediatr. 1990. PMID: 2373114
-
Glycogen storage disease type I. Results of treatment with frequent daytime feeding, combined with nocturnal intragastric feeding and with administration of an alpha-glucosidase inhibitor.Eur J Pediatr. 1983 Apr;140(2):102-4. doi: 10.1007/BF00441652. Eur J Pediatr. 1983. PMID: 6411473
-
Glycogenosis type Ib complicated by severe granulocytopenia resembling inherited neutropenia.Eur J Pediatr. 1981 Sep;137(1):81-4. doi: 10.1007/BF00441175. Eur J Pediatr. 1981. PMID: 6944203 No abstract available.
-
Hyperuricemia in glycogen storage disease type I. Contributions by hypoglycemia and hyperglucagonemia to increased urate production.J Clin Invest. 1985 Jan;75(1):251-7. doi: 10.1172/JCI111681. J Clin Invest. 1985. PMID: 2856925 Free PMC article.