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. 2016 May-Jun;61(3):348.
doi: 10.4103/0019-5154.182472.

Ross Syndrome: A Case Report and Review of Cases from India

Manoj Kumar Agarwala  1 , Leni George  1 , Harshad Parmar  2 , Vivek Mathew  3
Affiliations

Ross Syndrome: A Case Report and Review of Cases from India

Manoj Kumar Agarwala et al. Indian J Dermatol. 2016 May-Jun.

Abstract

Ross syndrome is a rare dysautonomia characterized by a clinical complex of segmental anhidrosis or hypohidrosis, areflexia, and tonic pupils. A very few cases (≃50) have been reported in literature since its original description in 1958. Here, we report the case of a middle-aged homemaker from Odisha, India, who presented with complaints of segmental hypohidrosis for the past 7 years.

Keywords: Holmes–Adie syndrome; India; Ross syndrome; hypohidrosis.

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Figures

Figure 1
Figure 1
Loss of sweating in the right side with hyperhidrosis on the left side predominantly involving the skin over T6-8 vertebral region
Figure 2
Figure 2
Sluggish pupillary reaction
Figure 3
Figure 3
Hyperhidrotic region showing dense eccrine glands units associated with lobules of mature adipocytes
Figure 4
Figure 4
Hypohidrotic skin on the right side showing sparse eccrine glands
See this image and copyright information in PMC

References

    1. Ross AT. Progressive selective sudomotor denervation; a case with coexisting Adie's syndrome. Neurology. 1958;8:809–17. - PubMed
    1. Nolano M, Provitera V, Perretti A, Stancanelli A, Saltalamacchia AM, Donadio V, et al. Ross syndrome: A rare or a misknown disorder of thermoregulation? A skin innervation study on 12 subjects. Brain. 2006;129(Pt 8):2119–31. - PubMed
    1. Luong M, Jomir L, Labauge P, Dandurand M, Meunier L, Stoebner PE. Ross syndrome with sweating anomaly associated with Sjögren syndrome: An infrared thermo-graphic case study. Acta Derm Venereol. 2011;91:80–1. - PubMed
    1. Vasudevan B, Sawhney M, Vishal S. Ross syndrome with ana positivity: A clue to possible autoimmune origin and treatment with intravenous immunoglobulin. Indian J Dermatol. 2010;55:274–6. - PMC - PubMed
    1. Nolano M, Provitera V, Donadio V, Stancanelli A, Saltalamacchia A, Caporaso G, et al. Ross syndrome: A lesson from a monozygotic twin pair. Neurology. 2013;80:417–8. - PubMed

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