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Case Reports
. 2016 Jun;49(3):210-3.
doi: 10.5090/kjtcs.2016.49.3.210. Epub 2016 Jun 5.

Life-Threatening Congenital Cystic Adenomatoid Malformation in the Premature Neonate

Yooyoung Chong  1 , Youn Ju Rhee  1 , Sung Joon Han  1 , Hyun Jin Cho  1 , Shin Kwang Kang  1 , Min-Woong Kang  1
Affiliations
Case Reports

Life-Threatening Congenital Cystic Adenomatoid Malformation in the Premature Neonate

Yooyoung Chong et al. Korean J Thorac Cardiovasc Surg. 2016 Jun.

Abstract

Congenital cystic adenomatoid malformation is a rare, but well-known disease. It can be managed conservatively in patients without symptoms or require surgical removal when symptomatic. The surgical option of choice is en bloc resection of the affected lesion. We report an experience of life-threatening congenital cystic adenoid malformation in a low-birth-weight (1,590 g) premature neonate who was successfully treated with a lobectomy of the lung.

Keywords: Cystic adenomatoid malformation of lung, congenital; Infant, low birth weight; Infant, premature.

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Figures

Fig. 1
Fig. 1
(A) Chest PA radiography (PA) at birth. There are no specific findings in either lung. (B) Chest PA radiography at day 9 of life. Hyperlucent lesions appear in the right lung field. (C) Chest PA radiography at day 20 of life. (D) Chest PA radiography on the day of surgery. Mediastinal deviation and hyperlucent lesions appear in the right lower lung field. PA, posterior-anterior.
Fig. 2
Fig. 2
A chest computed tomography scan shows multiple thin-walled cysts in the right middle lobe.
Fig. 3
Fig. 3
Bulging out of the right middle lobe after thoracotomy with cystic change.
See this image and copyright information in PMC

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