[Primary multinodular panniculitis or fat necrosis in children]

Abstract

The authors report 4 cases of primary multinodular panniculitis. One was a typical Weber-Christian syndrome; the clinical picture of the others was intermediate between the Weber-Christian syndrome and the Rothmann-Makaï syndrome. A pancreatic or an enzymatic disorder were excluded. The hypothesis of an abnormal fragility of adipose tissue or of a failure in the mechanisms of protection against lipophagia is raised.