Nonmalignant Adult Thoracic Lymphatic Disorders

Abstract

The thoracic lymphatic disorders are a heterogeneous group of uncommon conditions that are associated with thoracic masses, interstitial pulmonary infiltrates, and chylous complications. Accurate diagnosis of the thoracic lymphatic disorders has important implications for the newest approaches to management, including embolization and treatment with antilymphangiogenic drugs. New imaging techniques to characterize lymphatic flow, such as dynamic contrast-enhanced magnetic resonance lymphangiogram, are redefining approaches to disease classification and therapy.

Keywords: Generalize lymphatic anomaly (GLA); Gorham-Stout disease (GSD); Kaposiform lymphangiomatosis (KL); Lymphangiectasia; Lymphangioma; Lymphangiomatosis; Pulmonary lymphangiectasia; Yellow nail syndrome.