Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
. 2016 Jul 13:5:1680.
doi: 10.12688/f1000research.8823.2. eCollection 2016.

Case Report: ALCAPA syndrome: successful repair with an anatomical and physiological alternative surgical technique

Luis Gustavo Vilá Mollinedo  1 , Andrés Jaime Uribe  1 , José Luis Aceves Chimal  1 , Roberto Pablo Martínez-Rubio  1 , Karen Patricia Hernández-Romero  1
Affiliations

Case Report: ALCAPA syndrome: successful repair with an anatomical and physiological alternative surgical technique

Luis Gustavo Vilá Mollinedo et al. F1000Res. .

Abstract

Anomalous left coronary artery from the pulmonary artery, or ALCAPA syndrome, is a rare congenital cardiac disease that can cause myocardial infarction, heart failure and even death in paediatric patients. Only few untreated patients survive until adult age. Here we present the case of a 33-year-old female patient with paroxysmal tachycardia, syncope and mild exertional dyspnoea. She was diagnosed with ALCAPA syndrome and underwent surgical correction with an alternative technique of left main coronary artery extension to the aorta.

Keywords: ALCAPA syndrome; Adults with ALCAPA; Bland-White-Garland syndrome; Coronary extension technique; Coronary vessel anomalies.

PubMed Disclaimer

Conflict of interest statement

Competing interests: No competing interests were disclosed.

Figures

Figure 1.
Figure 1.
A – Arrow – RCA dilated arising from the aorta. B – Arrow – LMA arising from lateral aspect of the MPA.
Figure 2.
Figure 2.. AngioCAT – Arrow – Adequate graft patency (combined pulmonary tissue and bovine pericardium patch).
Figure 3.
Figure 3.
A – LMA taken from the MPA and reconstructed as a tubular structure with bovine pericardium. B – LMA anastomosis to the Ao as in a normal position, MPA reconstructed with a pericardial patch. C – MPA reconstructed with a Dacron graft.
Figure 4.
Figure 4.. ALCAPA syndrome pathophysiology.
See this image and copyright information in PMC

References

    1. Safaa AM, Du LL, Batra R: A rare case of adult type ALCAPA syndrome: presentation, diagnosis and management. Heart Lung Circ. 2013;22(6):444–446. 10.1016/j.hlc.2012.10.011 - DOI - PubMed
    1. Alsoufi B, Sallehuddin A, Bulbul Z, et al. : Surgical strategy to establish a dual-coronary system for the management of anomalous left coronary artery origin from the pulmonary artery. Ann Thorac Surg. 2008;86(1):170–176. 10.1016/j.athoracsur.2008.03.032 - DOI - PubMed
    1. Guo HW, Xu JP, Song YH, et al. : Repair of anomalous origin of left coronary artery from the pulmonary artery. Asian Cardiovasc Thorac Ann. 2007;15(3):240–242. 10.1177/021849230701500314 - DOI - PubMed
    1. Mohanty SR, Murthy KS, Varghese R, et al. : Evolution of surgical strategies for anomalous left coronary artery. Asian Cardiovasc Thorac Ann. 2001;9(4):269–274. 10.1177/021849230100900405 - DOI
    1. Murala JS, Sankar MN, Agarwal R, et al. : Anomalous origin of left coronary artery from pulmonary artery in adults. Asian Cardiovasc Thorac Ann. 2006;14(1):38–42. 10.1177/021849230601400110 - DOI - PubMed

LinkOut - more resources