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Review
. 2016 Sep;11(3):262-270.
doi: 10.1177/1558944715614857. Epub 2016 Sep 1.

Symbrachydactyly

Parker B Goodell  1 , Andrea S Bauer  2 , Francisco J A Sierra  3 , Michelle A James  2
Affiliations
Review

Symbrachydactyly

Parker B Goodell et al. Hand (N Y). 2016 Sep.

Abstract

Background: Symbrachydactyly is a unilateral congenital hand malformation characterized by failure of formation of fingers and the presence of rudimentary digit nubbins. The management is variable and are investigated in this review. Methods: A detailed review of the literature was compiled into succinct clinically relevant categories. Results: Etiology, classification, non-surgical management, surgical intervention, and patient oriented outcomes are discussed. Conclusions: All interventions should prioritize realistic, evidence-supported appearance and functional gains. Studies of the baseline function and quality of life of children with symbrachydactyly would allow surgeons to better understand functional changes associated with various interventions and would help surgeons and parents to make the best treatment decisions.

Keywords: Poland syndrome; congenital hand; symbrachydactyly.

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Conflict of interest statement

The author(s) declared no potential conflicts of interest with respect to the research, authorship, and/or publication of this article.

Figures

Figure 1.
Figure 1.
A typical hand with symbrachydactyly.
Figure 2.
Figure 2.
The chest in Poland syndrome, with hypoplasia of the pectoralis major muscle.
Figure 3.
Figure 3.
The spectrum of symbrachydactyly as classified by Foucher: (a) type I, (b) type IIA, (c) type IIB, (d) type IIC, (e) type IIIA, (f) type IIIB, (g) type IVA, and (h) type IVB. Note. A description of each type is listed in Table 2.
Figure 4.
Figure 4.
A patient with symbrachydactyly wearing an opposition paddle.
Figure 5.
Figure 5.
Fourfold Z-plasty to open the web space of the patient with type IIC symbrachydactyly. (a) Preoperative planning of the flaps. (b) Postoperative appearance.
Figure 6.
Figure 6.
A dorsal rotational flap for more severe deficiency of the first web space. (a) Preoperative and (b) Postoperative.
Figure 7.
Figure 7.
(a) Preoperative and (b) postoperative radiographs of nonvascularized toe phalanx transfers.
See this image and copyright information in PMC

References

    1. Andersson GB, Gillberg C, Fernell E, Johansson M, Nachemson A. Children with surgically corrected hand deformities and upper limb deficiencies: self-concept and psychological well-being. J Hand Surg Eur Vol. 2011;36(9):795-801. - PubMed
    1. Bavinck JN, Weaver DD. Subclavian artery supply disruption sequence: hypothesis of a vascular etiology for Poland, Klippel-Feil, and Möbius anomalies. Am J Med Genet. 1986;23(4):903-918. - PubMed
    1. Bellew M, Haworth J, Kay SP. Toe to hand transfer in children: ten year follow up of psychological aspects. J Plast Reconstr Aesthet Surg. 2011;64(6):766-775. - PubMed
    1. Blauth W, Gekeler J. [Morphology and classification of symbrachydactyly]. Handchirurgie. 1971;3(4):123-128. - PubMed
    1. Bouvet JP, Leveque D, Bernetieres F, Gros JJ. Vascular origin of Poland syndrome? a comparative rheographic study of the vascularisation of the arms in eight patients. Eur J Pediatr. 1978;128(1):17-26. - PubMed

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