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Review
. 2016 Oct 1;43(5):437-440.
doi: 10.14503/THIJ-15-5320. eCollection 2016 Oct.

Asymptomatic Interrupted Aortic Arch, Severe Tricuspid Regurgitation, and Bicuspid Aortic Valve in a 76-Year-Old Woman

Masih Tajdini, Akram Sardari, Seyed Khalil Forouzannia, Abdolvahab Baradaran, Seyed Mohammad Reza Hosseini, Seyed Ebrahim Kassaian
Review

Asymptomatic Interrupted Aortic Arch, Severe Tricuspid Regurgitation, and Bicuspid Aortic Valve in a 76-Year-Old Woman

Masih Tajdini et al. Tex Heart Inst J. .

Abstract

Interrupted aortic arch is a rare congenital abnormality with a high infancy mortality rate. The principal finding is loss of luminal continuity between the ascending and descending portions of the aorta. Because of the high mortality rate in infancy, interrupted aortic arch is very rare among adults. In this report, we describe the case of a 76-year-old woman with asymptomatic interrupted aortic arch, severe tricuspid regurgitation, and bicuspid aortic valve. To our knowledge, she is the oldest patient ever reported with this possibly unique combination of pathologic conditions. In addition to reporting her case, we review the relevant medical literature.

Keywords: Adult; aorta, thoracic/abnormalities; aortic valve/abnormalities; arteriovenous malformations/diagnosis/surgery; heart defects, congenital; tricuspid valve/pathology; vascular malformations/physiopathology.

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Figures

Fig. 1
Fig. 1
Aortogram shows a bicuspid aortic valve and no contrast medium passing through the descending aorta after aortic root injection.
Fig. 2
Fig. 2
Computed tomographic angiograms (3-dimensional reconstruction) of the aorta show A) collateral circulation between the aortic arch and the descending aorta and B), in left posterior view, occlusion of the aorta (arrow) immediately distal to the left subclavian artery.
See this image and copyright information in PMC

References

    1. Bugan B, Iyisoy A, Celik M, Kucuk U, Boz U, Celik T. Isolated type A interrupted aortic arch in an asymptomatic 19-year-old man. Tex Heart Inst J. 2011;38(5):559–61. - PMC - PubMed
    1. Ponte M, Dias A, Dias Ferreira N, Fonseca C, Mota JC, Gama V. Interrupted aortic arch: a misdiagnosed cause of hypertension. Rev Port Cardiol. 2014;33(6):389.e1–5. - PubMed
    1. Hokenek F, Sever K, Ugurlucan M, Sakliyan M, Kinoglu B. Interrupted aortic arch in adulthood. Thorac Cardiovasc Surg. 2008;56(3):140–2. - PubMed
    1. Messner G, Reul GJ, Flamm SD, Gregoric ID, Opfermann UT. Interrupted aortic arch in an adult: single-stage extra-anatomic repair. Tex Heart Inst J. 2002;29(2):118–21. - PMC - PubMed
    1. Collins-Nakai RL, Dick M, Parisi-Buckley L, Fyler DC, Castaneda AR. Interrupted aortic arch in infancy. J Pediatr. 1976;88(6):959–62. - PubMed

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