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Case Reports
. 2016 Sep;10(9):OD15-OD17.
doi: 10.7860/JCDR/2016/21623.8547. Epub 2016 Sep 1.

Left Pulmonary Agenesis with Right Lung Bronchiectasis in an Adult

Prabhat Kumar  1 , Ghazal Tansir  2 , Gargi Sasmal  2 , Juhi Dixit  2 , Ratnakar Sahoo  3
Affiliations
Case Reports

Left Pulmonary Agenesis with Right Lung Bronchiectasis in an Adult

Prabhat Kumar et al. J Clin Diagn Res. 2016 Sep.

Abstract

Pulmonary agenesis is a rare congenital anomaly characterized by the absence of pulmonary parenchyma and vasculature. Bilateral pulmonary agenesis is incompatible with extrauterine life. Unilateral agenesis is often associated with other congenital cardiovascular, genitourinary and gastrointestinal malformations. Right lung agenesis is more frequently associated with congenital anomalies and has poor prognosis as compared to left lung agenesis. Diagnosis is often made in childhood but can be delayed, if the clinician is not aware about this entity. Chest radiograph in unilateral lung agenesis shows opaque hemithorax and these patients are often confused with other common causes of opaque hemithorax like collapse, pleural effusion and diaphragmatic hernia. We report a case of left lung agenesis with right lung bronchiectasis in a middle-aged adult who was treated for tuberculous pleural effusion and was referred to our institute for persistent symptoms despite treatment.

Keywords: Cor-pulmonale; Opaque hemithorax; Respiratory failure.

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Figures

[Table/Fig-1]:
[Table/Fig-1]:
Chest X ray showing opaque left hemithorax with mediastinal shift to left.
[Table/Fig-2]:
[Table/Fig-2]:
Transverse section of CT chest showing left lung agenesis and right lung bronchiectasis.
[Table/Fig-3]:
[Table/Fig-3]:
Coronal section of CT chest showing compensatory expansion of right lung with right lower lobe bronchiectasis.
[Table/Fig-4]:
[Table/Fig-4]:
CT pulmonary angiography showing absent pulmonary vasculature on left side.
[Table/Fig-5]:
[Table/Fig-5]:
Absent left pulmonary artery and elongated main pulmonary artery.
[Table/Fig-6]:
[Table/Fig-6]:
Absent left bronchus on bronchoscopy.
See this image and copyright information in PMC

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