Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2016 Oct 4;4(1):255.
doi: 10.2484/rcr.v4i1.255. eCollection 2009.

Asymptomatic Congenital Intrahepatic Portosystemic Shunt

Karen M Brown, Hassan Hal
Case Reports

Asymptomatic Congenital Intrahepatic Portosystemic Shunt

Karen M Brown et al. Radiol Case Rep. .

Abstract

Congenital (spontaneous) intrahepatic portosystemic shunt is rare in the English literature. Most cases of portosystemic shunt occur after trauma, surgery, liver biopsy or as a result of chronic portal hypertension. Chronic shunting may result in encephalopathy, bleeding or hyperinsulinism. We report a case of an asymptomatic adult female with a presumed congenital intrahepatic portosystemic shunt and discuss the pertinent imaging findings and important key concepts related to this condition.

Keywords: CT, computed tomography.

PubMed Disclaimer

Figures

Figure 1
Figure 1
48-year-old woman with congenital intrahepatic portosystemic shunt. (A-D) Axial enhanced CT images demonstrate the portal vein (red arrow) and middle hepatic vein (blue arrow) with a portosystemic shunt within the medial segment of the left hepatic lobe (purple arrow). Note also a striated left nephrogram (curved green arrow).
Figure 2
Figure 2
48-year-old woman with congenital intrahepatic portosystemic shunt. (A-D) Coronal enhanced CT images demonstrate branches of the portal vein (red arrow) and middle hepatic vein (blue arrow) with a portosystemic shunt within the medial segment of the left hepatic lobe (purple arrow).
Figure 3
Figure 3
48-year-old woman with congenital intrahepatic portosystemic shunt. (A-D) Transverse sonographic images through the liver demonstrate hepatopedal flow through the portal vein (PV) and hepatofugal flow through the middle hepatic vein (MHV) with turbulence within a portosystemic shunt within the left hepatic lobe.
See this image and copyright information in PMC

References

    1. Howard ER, Davenport M. Congenital extrahepatic portocaval shunts—the Abernethy malformation. J Pediatr Surg. 1997 Mar;32(3):494–497. [PubMed] - PubMed
    1. Oguz B, Akata D, Balkanci F, Akhan O. Intrahepatic portosystemic venous shunt: diagnosis by colour/power Doppler imaging and three-dimensional ultrasound. Br J Radiol. 2003 Jul;76(907):487–490. [PubMed] - PubMed
    1. Pocha C, Maliakkal B. Spontaneous intrahepatic portal-systemic venous shunt in the adult: case report and review of the literature. Dig Dis Sci. 2004 Aug;49(7-8):1201–1206. [PubMed] - PubMed
    1. Tanoue S, Kiyosue H, Komatsu E, Hori Y, Maeda T, Mori H. Symptomatic intrahepatic portosystemic venous shunt: angiographic findings and transcatheter embolization with an alternative approach. AJR Am J Roentgenol. 2003 Jul;181(1):71–78. [PubMed] - PubMed
    1. Park JH, Cha SH, Han JK, Han MC. Intrahepatic portosystemic venous shunt. AJR Am J Roentgenol. 1990 Sep;155(3):527–528. [PubMed] - PubMed

Publication types

LinkOut - more resources