Computerized tomography in primary hyperammonemia
- PMID: 2797431
- DOI: 10.1007/BF00344184
Computerized tomography in primary hyperammonemia
Abstract
Urea cycle enzymopathies are rare in the literature. They are accompanied by neurological disorders somehow related to the increase in blood ammonia. Reviewing the possible physiopathological course we present a case in which during an eight month period severe cerebral atrophy developed, more intense in the occipital region but totally sparing the posterior cranial fossa structures.