Systemic Sclerosis Sine Scleroderma in Mexican Patients. Case Reports
- PMID: 28065485
- DOI: 10.1016/j.reuma.2016.11.004
Systemic Sclerosis Sine Scleroderma in Mexican Patients. Case Reports
Abstract
Systemic sclerosis sine scleroderma (ssSSc) is a form of systemic sclerosis that is characterized by Raynaud's phenomenon (RP), visceral involvement without thickening of skin and anticentromere antibodies (ACA). We studied 10 ssSsc patients with a prevalence of 2%. The clinical signs were: RP 9/10, esophageal manifestations 8/10, pulmonary arterial hypertension 4/10, interstitial lung disease 4/10, cardiac signs 3/10 and ACA 8/10.
Conclusion: In patients with RP, esophageal dysmotility, interstitial lung disease and pulmonary arterial hypertension should be tested for ACA in order to establish a prompt diagnosis and treatment of ssSSc.
Keywords: Clinical manifestations; Esclerosis sistémica sin esclerodermia; Manifestaciones clínicas; Prevalence; Prevalencia; Systemic sclerosis sine scleroderma.
Copyright © 2016 Elsevier España, S.L.U. and Sociedad Española de Reumatología y Colegio Mexicano de Reumatología. All rights reserved.
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