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Case Reports
. 2014 Nov;17(4):150-152.
doi: 10.1002/j.2205-0140.2014.tb00237.x. Epub 2015 Dec 31.

Uhl's anomaly detected in-utero

Marta K Matic  1 , Rodney Kirsop  2 , Philippa A Ramsay  3
Affiliations
Case Reports

Uhl's anomaly detected in-utero

Marta K Matic et al. Australas J Ultrasound Med. 2014 Nov.

Abstract

Uhl's anomaly is rarely diagnosed antenatally. It is a condition characterised by partial or complete absence of the right ventricular myocardium and the heart conducting system. We present a case of Uhl's anomaly diagnosed during fetal life on prenatal ultrasound, with eight years postnatal follow-up.

Keywords: Uhl's anomaly; antenatal; fetal; ultrasound.

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Figures

Figure 1
Figure 1
Fetal echocardiograph showing gross cardiomegaly and a large aneurysmal segment in the free wall of the right ventricle.
See this image and copyright information in PMC

References

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