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Review
. 2017 Feb 14:2017:bcr2016218227.
doi: 10.1136/bcr-2016-218227.

Hepatopulmonary fusion: a rare and potentially lethal association with right congenital diaphragmatic hernia

Vishesh Jain  1 , Devendra Kumar Yadav  1 , Devasenathipathy Kandasamy  2 , Devendra Kumar Gupta  1
Affiliations
Review

Hepatopulmonary fusion: a rare and potentially lethal association with right congenital diaphragmatic hernia

Vishesh Jain et al. BMJ Case Rep. .

Abstract

Hepatopulmonary fusion is an extremely rare accompaniment of right congenital diaphragmatic hernia. It is associated with abnormal systemic arterial supply and venous drainage of the right lung along with congenital heart disease. Children with this condition have a comparatively poor prognosis. We report a case of right congenital diaphragmatic hernia with hepatopulmonary fusion along with review of the literature with stress on diagnosis and management.

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Conflict of interest statement

Competing interests: None declared.

Figures

Figure 1
Figure 1
(A) Plain chest radiograph reveals opacity in right lower thorax continuous with the hepatic shadow suggestive of right eventration/diaphragmatic hernia. White arrowhead denotes the presence of ipsilateral mediastinal deviation. (B) Non-contrast CT confirms the finding of the chest radiograph.
Figure 2
Figure 2
Intraoperative photograph following separation of the lung and the liver. Presence of aberrant artery (white arrowhead) and aberrant vein (black arrowhead) is also noted. The right lung has been retracted.
See this image and copyright information in PMC

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References

    1. Akinkuotu AC, Cruz SM, Cass DL et al. . Revisiting outcomes of right congenital diaphragmatic hernia. J Surg Res 2015;198:413–7. 10.1016/j.jss.2015.03.090 - DOI - PubMed
    1. Duess JW, Zani-Ruttenstock EM, Garriboli M et al. . Outcome of right-sided diaphragmatic hernia repair: a multicentre study. Pediatr Surg Int 2015;31:465–71. 10.1007/s00383-015-3695-y - DOI - PubMed
    1. Olenik D, Codrich D, Gobbo F et al. . Hepatopulmonary fusion in a newborn. An uncommon intraoperatory finding during right congenital diaphragmatic hernia surgery: case description and review of literature. Hernia 2014;18:417–21. 10.1007/s10029-012-1042-y - DOI - PubMed
    1. Slovis TL, Farmer DL, Berdon WE et al. . Hepatic pulmonary fusion in neonates. Am J Roentgenol 2000;174:229–33. 10.2214/ajr.174.1.1740229 - DOI - PubMed
    1. Woodring JH, Howard TA, Kanga JF. Congenital pulmonary venolobar syndrome revisited. Radiogr Rev Publ Radiol Soc N Am 1994;14:349–69. - PubMed