The Lymphatic Circulation in Adaptations to the Fontan Circulation

Sabarinath Menon^{1

2

3}, Murthy Chennapragada^{3

4}, Shinya Ugaki^{1

3}, Gary F Sholler^{1

3

4}, Julian Ayer^{1

3

4}, David S Winlaw^{5

6

7}

Affiliations

¹ The Heart Centre for Children, The Children's Hospital at Westmead, Sydney, NSW, Australia.
² Sree Chitra Tirunal Institute of Medical sciences and Technology, Thiruvananthapuram, Kerala, 695,011, India.
³ Sydney Children's Hospital Network, The Children's Hospital at Westmead, 212 Hawkesbury Road, Westmead, NSW, 2145, Australia.
⁴ Discipline of Child and Adolescent Health, Sydney Medical School, University of Sydney, Camperdown, NSW, 2006, Australia.
⁵ The Heart Centre for Children, The Children's Hospital at Westmead, Sydney, NSW, Australia. david.winlaw@health.nsw.gov.au.
⁶ Sydney Children's Hospital Network, The Children's Hospital at Westmead, 212 Hawkesbury Road, Westmead, NSW, 2145, Australia. david.winlaw@health.nsw.gov.au.
⁷ Discipline of Child and Adolescent Health, Sydney Medical School, University of Sydney, Camperdown, NSW, 2006, Australia. david.winlaw@health.nsw.gov.au.

PMID: 28210768
DOI: 10.1007/s00246-017-1576-y

Review

The Lymphatic Circulation in Adaptations to the Fontan Circulation

Sabarinath Menon et al. Pediatr Cardiol. 2017 Jun.

. 2017 Jun;38(5):886-892.

doi: 10.1007/s00246-017-1576-y. Epub 2017 Feb 16.

Authors

Sabarinath Menon^{1

2

3}, Murthy Chennapragada^{3

4}, Shinya Ugaki^{1

3}, Gary F Sholler^{1

3

4}, Julian Ayer^{1

3

4}, David S Winlaw^{5

6

7}

Affiliations

¹ The Heart Centre for Children, The Children's Hospital at Westmead, Sydney, NSW, Australia.
² Sree Chitra Tirunal Institute of Medical sciences and Technology, Thiruvananthapuram, Kerala, 695,011, India.
³ Sydney Children's Hospital Network, The Children's Hospital at Westmead, 212 Hawkesbury Road, Westmead, NSW, 2145, Australia.
⁴ Discipline of Child and Adolescent Health, Sydney Medical School, University of Sydney, Camperdown, NSW, 2006, Australia.
⁵ The Heart Centre for Children, The Children's Hospital at Westmead, Sydney, NSW, Australia. david.winlaw@health.nsw.gov.au.
⁶ Sydney Children's Hospital Network, The Children's Hospital at Westmead, 212 Hawkesbury Road, Westmead, NSW, 2145, Australia. david.winlaw@health.nsw.gov.au.
⁷ Discipline of Child and Adolescent Health, Sydney Medical School, University of Sydney, Camperdown, NSW, 2006, Australia. david.winlaw@health.nsw.gov.au.

PMID: 28210768
DOI: 10.1007/s00246-017-1576-y

Abstract

Failing Fontan continues to be major problem for patients on the univentricular pathway. Failing Fontan is often complicated by chylothorax, plastic bronchitis and protein loosing enteropathy. The role of lymphatic circulation in Fontan circulation is still being researched. Newer imaging modalities give insight into the role of abnormal dilatation and retrograde flow in lymphatic channels post Fontan. Interventional strategies targeting abnormal lymphatic channels, provides an alternative management strategy for patients with failing Fontan. This review focuses on the role of lymphatic system in adaptations to Fontan circulation.

Keywords: Congenital heart disease; Fontan; Fontan failure; Lymphatic disorders; Lymphatics; Single ventricle physiology.

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References

1. Am Heart J. 2005 Sep;150(3):588-94 - PubMed
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1. Expert Rev Cardiovasc Ther. 2011 Jun;9(6):785-93 - PubMed
1. Pediatrics. 2003 Sep;112(3 Pt 1):e242-7 - PubMed
1. J Am Coll Cardiol. 2003 Sep 17;42(6):1061-5 - PubMed

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The Lymphatic Circulation in Adaptations to the Fontan Circulation

Affiliations

The Lymphatic Circulation in Adaptations to the Fontan Circulation

Authors

Affiliations

Abstract

References

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MeSH terms

LinkOut - more resources

Full Text Sources

Other Literature Sources

Medical