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Case Reports
. 2017:2017:5693501.
doi: 10.1155/2017/5693501. Epub 2017 Jan 30.

Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis

Kenan Barut  1 , Sezgin Sahin  1 , Amra Adrovic  1 , Velat Sen  2 , Ozgur Kasapcopur  1
Affiliations
Case Reports

Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis

Kenan Barut et al. Case Rep Pediatr. 2017.

Abstract

Macrophage activation syndrome, a severe complication of systemic juvenile idiopathic arthritis and other inflammatory diseases, represents one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis has been classically characterized by a triad of anemia, hemoptysis, and lung infiltrates on chest radiogram. Although the majority of patients of pulmonary hemosiderosis are considered idiopathic, secondary hemosiderosis associated with known diseases could be seen. In this case report, we aimed to present gradually increased pulmonary manifestations due to pulmonary hemosiderosis with recurrent macrophage activation syndrome attacks in a child with systemic juvenile idiopathic arthritis.

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Conflict of interest statement

The authors declare that there is no conflict of interests.

Figures

Figure 1
Figure 1
Bilateral lung interstitial infiltration in chest radiography.
Figure 2
Figure 2
Bilateral diffuse fibrous changes and reticulonodular opacities in chest tomogram.
See this image and copyright information in PMC

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