Clinical features and current management of chronic granulomatous disease
Affiliations
- PMID: 2839458
Item in Clipboard
Clinical features and current management of chronic granulomatous disease
Hematol Oncol Clin North Am.
1988 Jun.
Abstract
Chronic granulomatous disease (CGD) is a diverse disorder characterized by several clinical presentations and a multitude of metabolic defects. The authors summarize the clinical features and current management of CGD, offer a definition of the disease based on molecular defects of the respiratory burst, and present their experience with trimethoprim/sulfamethoxazole prophylaxis.
Similar articles
-
Cellular and molecular effects of recombinant interferon gamma in chronic granulomatous disease.Hematol Oncol Clin North Am. 1988 Jun;2(2):267-76. Hematol Oncol Clin North Am. 1988. PMID: 2839459
-
The respiratory burst oxidase.Hematol Oncol Clin North Am. 1988 Jun;2(2):201-12. Hematol Oncol Clin North Am. 1988. PMID: 2839456 Review.
-
Antibacterial prophylaxis in chronic granulomatous disease. A case report.Isr J Med Sci. 1983 Nov;19(11):1004-5. Isr J Med Sci. 1983. PMID: 6607239
-
Classification of chronic granulomatous disease.Hematol Oncol Clin North Am. 1988 Jun;2(2):241-52. Hematol Oncol Clin North Am. 1988. PMID: 2839457
-
Delineation of the phagocyte NADPH oxidase through studies of chronic granulomatous diseases of childhood.Int J Tissue React. 1993;15(3):99-103. Int J Tissue React. 1993. PMID: 8188451 Review.
Cited by
-
Mutations in the promoter region of the gene for gp91-phox in X-linked chronic granulomatous disease with decreased expression of cytochrome b558.J Clin Invest. 1994 Sep;94(3):1205-11. doi: 10.1172/JCI117437. J Clin Invest. 1994. PMID: 8083361 Free PMC article.
-
The cytosolic subunit p67phox contains an NADPH-binding site that participates in catalysis by the leukocyte NADPH oxidase.J Clin Invest. 1996 Aug 15;98(4):977-83. doi: 10.1172/JCI118882. J Clin Invest. 1996. PMID: 8770870 Free PMC article.
-
Effects of nitric oxide synthase inhibitors on murine infection with Mycobacterium tuberculosis.Infect Immun. 1995 Feb;63(2):736-40. doi: 10.1128/iai.63.2.736-740.1995. Infect Immun. 1995. PMID: 7529749 Free PMC article.
-
Hepatic abscess in patients with chronic granulomatous disease.Ann Surg. 2002 Mar;235(3):383-91. doi: 10.1097/00000658-200203000-00010. Ann Surg. 2002. PMID: 11882760 Free PMC article.
-
The p47phox mouse knock-out model of chronic granulomatous disease.J Exp Med. 1995 Sep 1;182(3):751-8. doi: 10.1084/jem.182.3.751. J Exp Med. 1995. PMID: 7650482 Free PMC article.