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Review
. 2017 May;30(5):23-27.
doi: 10.1097/01.JAA.0000515540.36581.92.

Keep them breathing: Cystic fibrosis pathophysiology, diagnosis, and treatment

Sheena D Brown  1 , Rachel White, Phil Tobin
Affiliations
Review

Keep them breathing: Cystic fibrosis pathophysiology, diagnosis, and treatment

Sheena D Brown et al. JAAPA. 2017 May.

Abstract

Cystic fibrosis (CF) affects more than 30,000 people in the United States and 80,000 people worldwide. This life-threatening genetic disorder causes a buildup of thick, viscous mucus secretions in various organ systems, most commonly the gastrointestinal, pulmonary, and genitourinary systems. This article reviews the clinical manifestations, diagnosis, and monitoring of patients with CF as well as guidelines for management and emerging pharmacologic treatments.

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