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Case Reports
. 2017 Jan-Jun;38(1):76-77.
doi: 10.4103/0253-7184.196891.

Extramammary Paget's disease of vulva: A rare entity

Sandhya Yadav  1 , Pratik Gahalaut  1 , Hardev Singh Soodan  1 , Nitin Mishra  1 , Madhur Kant Rastogi  1
Affiliations
Case Reports

Extramammary Paget's disease of vulva: A rare entity

Sandhya Yadav et al. Indian J Sex Transm Dis AIDS. 2017 Jan-Jun.

Abstract

Extramammary Paget's disease is a rare cutaneous, intraepithelial adenocarcinoma involving primarily the epidermis but occasionally extending into the underlying dermis. The condition typically presents as a red, velvety, pruritic skin rash of the vulva region which closely mimics a multitude of other, more common conditions. As a result, vulvar Paget's disease is frequently misdiagnosed, leading to an often lengthy lag time (an average of about 2-3 years) between the onset of symptoms and diagnosis.

Keywords: Genital malignancy; intraepithelial carcinoma; non-healing ulcer.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
A well-defined erythematous plaque
Figure 2
Figure 2
Numerous Paget's cells within the epidermis (H and E, ×40)
See this image and copyright information in PMC

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