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Case Reports
. 2017 May 1;8(3):19.
doi: 10.21699/ajcr.v8i3.568. eCollection 2017 May-Jun.

Thoracoschisis associated with Limb Body Wall Complex

Dragana Vujovic  1 , Aleksandar Sretenovic  1   2 , Maja Raicevic  3 , MarijaLukac MarijaLukac  1   2 , Tamara Krstajic  1 , Vesna Ljubic  4 , Sanja Sindjic Antunovic  1   2
Affiliations
Case Reports

Thoracoschisis associated with Limb Body Wall Complex

Dragana Vujovic et al. APSP J Case Rep. .

Abstract

Thoracoschisis is a rare condition. A female newborn presented with right-sided thoracoschisis, associated with diaphragmatic hernia and protrusion of an accessory liver lobe through the chest wall defect along with deformity of the right forearm and hand duplication. Diagnosed as part of the limb-body wall complex (LBWC), management included resection of the exteriorized liver lobe followed by right hemidiaphragm and thoracic wall reconstruction.

Keywords: Limb deformity; Newborn; Riedel lobe; Thoracoschisis.

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Figures

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Figure 1: A) Eviscerated Riedel lobe.
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Figure 2: A) CT scan of liver showing liver protrusion through the thoracic wall defect.
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Figure 3: A)CT scan of right limb deformity.
See this image and copyright information in PMC

References

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