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. 2017 Apr-Jun;39(2):163-166.
doi: 10.1016/j.bjhh.2017.02.006. Epub 2017 Mar 11.

Sickle cell intrahepatic cholestasis unresponsive to exchange blood transfusion: a case report

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Sickle cell intrahepatic cholestasis unresponsive to exchange blood transfusion: a case report

Juliana Albano de Guimarães et al. Rev Bras Hematol Hemoter. 2017 Apr-Jun.
No abstract available

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Figures

Figure 1
Figure 1
(A) Axial T2 weighted magnetic resonance imaging of the abdomen showing liver enlargement with increased left (LL) and caudate (CL) lobes, associated to slightly irregular contours (arrows). (B) Magnetic resonance cholangiopancreatography showing normal gallbladder and slight focal dilatation of the biliary tree (arrows) in the right hepatic lobe without biliary obstruction.
Figure 2
Figure 2
(A) Evolution of albumin (g/dL), hemoglobin (g/dL) and international normalized ratio (INR) during hospitalization. (B) Evolution of direct and indirect bilirubin levels (mg/dL), aspartate aminotransferase (AST - U/L) and alanine aminotransferase (ALT - U/L) during hospitalization. Narrow arrows refer to red blood cell transfusions and the wide arrow indicates exchange blood transfusion (EBT).

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