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Case Reports
. 2017 Mar;27(2):193-196.
doi: 10.4314/ejhs.v27i2.12.

Combination of Encephalo-Myo-Pial-Synangiosis and Encephalo-Arterio-Pial-Synangiosis Procedure in Pediatric Moya-Moya Disease

Prastiya Gunawan  1 , Wihasto Suryaningtyas  1 , Darto Saharso  1 , Risky Prasetyo  1
Affiliations
Case Reports

Combination of Encephalo-Myo-Pial-Synangiosis and Encephalo-Arterio-Pial-Synangiosis Procedure in Pediatric Moya-Moya Disease

Prastiya Gunawan et al. Ethiop J Health Sci. 2017 Mar.

Abstract

Background: Moya-moya disease in children is a cerebrovascular disorder that may cause cerebral ischemic or hemorrhage.

Case details: We report an 8-year-old boy that was admitted with the chief complaint of repeated sudden half left body paralyze. MRA showed acute thrombotic infarction in the right hemisphere and internal carotid artery stenosis in the form of puffs of smokes. Indirect revascularization surgical procedure with combination of Encephalo-myo-pial-synangiosis (EMS) and Encephalo-arterio-pial-synangiosis (EAS) was performed. It resulted in a good response.

Conclusion: Moya-moya disease can lead to permanent neurological disability if untreated. Satisfactory outcome was noted following combination surgery management with EMS and EAS.

Keywords: Encephalo-arterio-pial-synangiosis; Encephalo-myo-pial-synangiosis; Moya-moya disease; children.

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Figures

Figure 1
Figure 1
Head MRI showing infarction in right temporal region and encephalomalacia cyst in right temporal region
Figure 2
Figure 2
Head MRA showing puff of smokes
See this image and copyright information in PMC

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