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Case Reports
. 2017 May-Jun;8(3):195-197.
doi: 10.4103/idoj.IDOJ_51_16.

Dermatofibrosarcoma Protuberans in a 9-Year-Old Child

Priyanka Patil  1 , Swagata Tambe  1 , Chitra Nayak  1 , C Ramya  1
Affiliations
Case Reports

Dermatofibrosarcoma Protuberans in a 9-Year-Old Child

Priyanka Patil et al. Indian Dermatol Online J. 2017 May-Jun.

Abstract

Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue neoplasm of low-to-intermediate grade malignant potential. Childhood onset of DFSP is rare. It is most commonly seen on the trunk and proximal extremities. In children, a high index of suspicion is necessary to avoid delays in diagnosis that can lead to further morbidity. Here, we report a case of DFSP in a 9-year-old female child. Excision biopsy of lesion was performed with 1 cm margin. After confirmation of the diagnosis by histopathology, the patient was observed for recurrence, but there was no recurrence after 1 and half years of follow up.

Keywords: Cartwheel pattern; Mohs micrographic surgery; children; dermatofibrosarcoma protuberans.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Single dark red tender 4 × 3 cm firm swelling with smooth telangiectatic surface present on the left shoulder
Figure 2
Figure 2
(a and b) Histopathology revealing spindle-shaped cells in storiform pattern and lymphohistiocytic infiltrate in dermis extending into the subcutaneous tissue giving honey comb appearance (H and E, a: ×400 and b: ×100)
Figure 3
Figure 3
Histopathology revealing mitoses less than 5 per 10 high power fields which differentiated from dermatofibroma (H and E, ×400)
See this image and copyright information in PMC

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