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Book

Right Aortic Arches

Mark A. Law  1 , Jay Mohan  2
In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2025 Jan.
.
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Book

Right Aortic Arches

Mark A. Law et al.
Free Books & Documents

Excerpt

Right aortic arch anomalies occur in 0.01 to 0.1% of the general population. Abnormalities of aortic arch branching and orientation are associated with a variety of congenital heart defects (tetralogy of Fallot and truncus arteriosus), as well as chromosomal abnormalities, such as DiGeorge syndrome (22q11 deletion). While a right aortic arch with mirror image branching of the head and neck vessels does not cause any physiologic cardiovascular effects, a right aortic arch can be associated with other congenital heart defects. A subset of right aortic arches with certain nonmirror image branching patterns of the head and neck vessels can be associated with a vascular ring. There are scenarios where the anatomic features of a right aortic are clinically relevant.

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Conflict of interest statement

Disclosure: Mark Law declares no relevant financial relationships with ineligible companies.

Disclosure: Jay Mohan declares no relevant financial relationships with ineligible companies.

References

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