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Case Reports
. 2017 Jul 12:10:233-236.
doi: 10.2147/IMCRJ.S125988. eCollection 2017.

Asymptomatic multinodular splenoma (splenic hamartoma) in a child with sickle cell anemia

Narcisse Elenga  1 , Sylvain Labbé  2 , Nicolas Leduc  2 , Anicet Sika  1 , Emma Cuadro  1 , Laurence Long  1 , Falucar Njuieyon  1 , Rémi Kom-Tchameni  1 , Thierry Basset  1
Affiliations
Case Reports

Asymptomatic multinodular splenoma (splenic hamartoma) in a child with sickle cell anemia

Narcisse Elenga et al. Int Med Case Rep J. .

Abstract

Splenoma is a rare and benign malformation usually fortuitously diagnosed during imaging, surgery or, unfortunately, at autopsy. Although splenoma was first described in 1861, its association with hematological pathology is a very unusual condition in children. We report the case of an asymptomatic splenoma in an 8-year-old boy with sickle cell anemia, whose diagnosis was confirmed after conventional splenectomy.

Keywords: child; conventional splenectomy; multinodular splenoma; sickle cell anemia.

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Conflict of interest statement

Disclosure The authors report no conflicts of interest in this work.

Figures

Figure 1
Figure 1
Multiple splenic nodules.
Figure 2
Figure 2
Endothelial cells are CD31- and CD8-positive. Notes: (A) CD31, arrow indicates positive endothelial cells. (B) CD8, arrows indicate positive endothelial cells. Abbreviation: CD, cluster of differentiation.
Figure 3
Figure 3
Vascular channels are CD34+. Notes: (A) Capillary proliferation in microscopy; (B) CD34; arrows indicate positive endothelial cells. Abbreviation: CD, cluster of differentiation.
Figure 4
Figure 4
Vascular channels are HHV8-negative. Abbreviation: HHV8, human herpesvirus 8.
See this image and copyright information in PMC

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