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. 2016 Sep;17(3):165-168.
doi: 10.7181/acfs.2016.17.3.165. Epub 2016 Sep 23.

Recurrent Extranodal NK/T-Cell Lymphoma Presenting as a Perforating Palatal Ulcer and Oro-Nasal Fistula

Kang Gyun Park  1 , Eun Sang Dhong  1 , Sik Namgoong  1 , Jung Kyu Han  1 , Seung Kyu Han  1 , Woo Kyung Kim  1
Affiliations

Recurrent Extranodal NK/T-Cell Lymphoma Presenting as a Perforating Palatal Ulcer and Oro-Nasal Fistula

Kang Gyun Park et al. Arch Craniofac Surg. 2016 Sep.

Abstract

Nasal-type extranodal natural killer/T-cell lymphoma (ENKTL) is a rare disease presenting with non-specific symptoms, typically originating in the nasal cavity, palate, or midfacial region. Oral cavity is an extremely rare site for this type of lymphoma. In this report, we present a case of palatal perforation and oro-nasal fistula as a manifestation of recurrent ENKTL. Complicated disease entity should be considered when surgeons deal with palatal perforation and oro-nasal fistula.

Keywords: Extranodal NK-T-cell lymphoma; Oral fistula; Palate.

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Conflict of interest statement

No potential conflict of interest relevant to this article was reported.

Figures

Fig. 1
Fig. 1. Computed tomography images of the midface reveals mucosal thickening in the left maxillary sinus and incomplete obstructions of both nasal cavities with hypertrophied conchae.
Fig. 2
Fig. 2. Nasal endoscopic examination reveals hypertrophic turbinate with minimal mucosa ulceration and bleeding in left nasal cavity.
Fig. 3
Fig. 3. The 1.5 cm×1.5 cm palatal perforation with resultant oro-nasal fistula.
Fig. 4
Fig. 4. Immunohistochemical staining is positive for extranodal natural killer/T-cell lymphoma marker in the atypical lymphoid cells (CD56, ×200).
See this image and copyright information in PMC

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