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Case Reports
. 2018 Jun;59(6):1494-1497.
doi: 10.1080/10428194.2017.1382697. Epub 2017 Sep 28.

Pulmonary veno-occlusive disease in a pediatric hematopoietic stem cell transplant patient: a cautionary tale

M S Zinter  1   2 , A Melton  1   3 , A J Sabnis  1   4 , C C Dvorak  1   3 , B M Elicker  5 , H M Nawaytou  1   6 , R J Kameny  1   2 , J R Fineman  1   2
Affiliations
Case Reports

Pulmonary veno-occlusive disease in a pediatric hematopoietic stem cell transplant patient: a cautionary tale

M S Zinter et al. Leuk Lymphoma. 2018 Jun.
No abstract available

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Conflict of interest statement

Conflict of Interest Statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1. Echocardiogram showing findings typical of pulmonary veno-occlusive disease
(A) Echocardiographic findings demonstrating right atrial and right ventricular dilation without left atrial dilation. There is also a small pericardial effusion. Tricuspid valve inflow Doppler showed right ventricular systolic pressure estimation of 55 mmHg above the right atrial pressure. Concomitant systemic blood pressure is annotated on the image (100/59 mmHg). (B) Two dimensional echocardiographic image of a moderately dilated inferior vena cava (2 cm). There was no collapse of the IVC with forced inspiration. This is suggestive of a right atrial pressure of 5–10 mmHg.
Figure 2
Figure 2. Contrast enhanced chest CT showing findings typical of pulmonary veno-occlusive disease
Axial (A) and sagittal reformatted (B) CT images demonstrate diffuse interlobular septal thickening (black arrows). Also visible are diffuse ground glass opacities and ill-defined centrilobular nodules.
See this image and copyright information in PMC

References

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