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Book

Sturge-Weber Syndrome

Achint K. Singh  1 , Michael Keenaghan  2
In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2025 Jan.
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Book

Sturge-Weber Syndrome

Achint K. Singh et al.
Free Books & Documents

Excerpt

Sturge-Weber syndrome (SWS) is a neurocutaneous syndrome characterized by angiomas involving the face, choroid, and leptomeninges. The facial capillary vascular malformation is also known as "port-wine stain" or "nevus flammeus" and usually is seen in the territory of the trigeminal nerve. Sturge-Weber syndrome is also called encephalotrigeminal angiomatosis. It is the third most common neurocutaneous syndrome after neurofibromatosis and tuberous sclerosis. The neurologic manifestations of SWS include atonic, tonic, or myoclonic seizures.

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Conflict of interest statement

Disclosure: Achint Singh declares no relevant financial relationships with ineligible companies.

Disclosure: Michael Keenaghan declares no relevant financial relationships with ineligible companies.

References

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