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Book

Supravalvar Aortic Stenosis

Mohinder R. Vindhyal, Shivani Priyadarshni  1 , Freidy Eid  2
In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2025 Jan.
.
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Book

Supravalvar Aortic Stenosis

Mohinder R. Vindhyal et al.
Free Books & Documents

Excerpt

Supravalvular aortic stenosis(SVAS) is a congenital heart defect. As the name suggests, SVAS means the section of the aorta located just above the aortic valve is narrowed. SVAS accounts for 8% to 14% of all congenital aortic stenosis. Three different types of SVAS are recognized: hourglass, membranous, and hypoplasia of aortic arch. Hourglass type SVAS is the most common. Membranous type is the result of the fibrous and/or fibromuscular semicircular diaphragm with a small central opening stretched across the aortic lumen. Diffuse hypoplasia of the ascending aorta is the third.[4]

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Conflict of interest statement

Disclosure: Mohinder Vindhyal declares no relevant financial relationships with ineligible companies.

Disclosure: Shivani Priyadarshni declares no relevant financial relationships with ineligible companies.

Disclosure: Freidy Eid declares no relevant financial relationships with ineligible companies.

References

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    1. Carr M, Curtis S, Marek J. EDUCATIONAL SERIES IN CONGENITAL HEART DISEASE: Congenital left-sided heart obstruction. Echo Res Pract. 2018 Jun;5(2):R23-R36. - PMC - PubMed
    1. Yuan SM. Congenital heart defects in Williams syndrome. Turk J Pediatr. 2017;59(3):225-232. - PubMed
    1. Morris CA. Williams Syndrome. In: Adam MP, Feldman J, Mirzaa GM, Pagon RA, Wallace SE, Amemiya A, editors. GeneReviews® [Internet] University of Washington, Seattle; Seattle (WA): 1999. Apr 9, - PubMed

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