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Case Reports
. 2017;92(5 Suppl 1):56-58.
doi: 10.1590/abd1806-4841.20175522.

Cutaneous manifestations of Churg-Strauss syndrome: key to diagnosis

Affiliations
Case Reports

Cutaneous manifestations of Churg-Strauss syndrome: key to diagnosis

Camila Carneiro Marques et al. An Bras Dermatol. 2017.

Abstract

Churg-Strauss syndrome is a rare systemic vasculitis characterized by asthma and other allergy symptoms as well as eosinophilia and necrotizing vasculitis involving small and medium-sized vessels. Its prevalence in the general population ranges from 1-3 cases per million a year, varying according to the population studied. The authors describe a case of a female patient affected by the disease with important systemic manifestations and not very florid skin lesions.

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Conflict of interest statement

Conflict of interest: None

Figures

Figure 1
Figure 1
Erythematous, purpuric papules with overlying erosions and crusts on the elbow
Figure 3
Figure 3
Erythematous, purpuric papules on the lateral aspect of the left foot
Figure 4
Figure 4
Multiple changes of the small vessels with foci of fibrin deposition. Leukocytoclasis. Malformed granuloma with interspersed eosinophils (Hematoxylin & eosin, X20 and X400)
Figure 2
Figure 2
Erythematous, purpuric papules on the dorsum of the left hand

References

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