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Review
. 2018 Jan;41(1):131-136.
doi: 10.1002/clc.22775. Epub 2018 Jan 29.

Subvalvular aortic stenosis: a review of current literature

Subodh R Devabhaktuni  1 , Eyas Chakfeh  2 , Ali O Malik  2 , Joshua A Pengson  2 , Jibran Rana  2 , Chowdhury H Ahsan  1
Affiliations
Review

Subvalvular aortic stenosis: a review of current literature

Subodh R Devabhaktuni et al. Clin Cardiol. 2018 Jan.

Abstract

Subvalvular aortic stenosis (SAS) is one of the common adult congenital heart diseases, with a prevalence of 6.5%. It is usually diagnosed in the first decade of life. Echocardiography is the test of choice to diagnose SAS. Surgical correction is the best treatment modality, and the prognosis is usually excellent. In this review, we describe the pathophysiology, diagnosis, prognosis, and management of SAS with a focus on different pathophysiologic mechanisms, diagnostic approach, and prognosis of the disease by reviewing the current literature.

Keywords: Review; Subaortic Stenosis; Subvalvular Aortic Stenosis.

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Conflict of interest statement

The authors declare no potential conflicts of interest.

Figures

Figure 1
Figure 1
Conceptual diagram describing each of these lesions. (A) Discrete subaortic membrane (arrows). (B) Thick fibromuscular ridge (arrows). (C) Tunnel or tubular (arrows). Abbreviations: AV, aortic valve; LA, left atrium; LV, left ventricle; MV, mitral valve; RV, right ventricle
Figure 2
Figure 2
Kaplan–Meier plots. (A) Survival and intervention‐free survival for patients with DSS and expected survival for the normal age‐matched Dutch population. (B) By sex.1 Abbreviations: DSS, discrete subvalvular aortic stenosis
Figure 3
Figure 3
Probability of postoperative AR over time. Abbreviations: AR, aortic regurgitation
See this image and copyright information in PMC

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