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. 2018 Mar 1;23(2):e225-e229.
doi: 10.4317/medoral.21319.

Beckwith-Wiedemann Syndrome: Open bite evolution after tongue reduction

E Alonso-Rodriguez  1 , E Gómez, M Martín, J-M Muñoz, J Hernández-Godoy, M Burgueño
Affiliations

Beckwith-Wiedemann Syndrome: Open bite evolution after tongue reduction

E Alonso-Rodriguez et al. Med Oral Patol Oral Cir Bucal. .

Abstract

Background: Macroglossia causes functional deficits such as airway obstruction, drooling, phonation difficulties, and leads to protrusion of dentoalveolar structures resulting in an anterior open bite and a prognathic mandibular appearance. Macroglossia is present in the majority of patients with Beckwith-Wiedemann syndrome (BWS) and surgical treatment may be indicated.

Material and methods: A retrospective review was conducted including BWS patients who underwent surgical tongue reduction between 2000 and 2015 at the Hospital Universitario La Paz, Madrid.

Results: Out of 16 patients with BWS, surgery was performed in 11 cases. Tongue protrusion with open bite was the main indication for surgical treatment. Reduction glossectomy was performed using the keyhole technique. We analysed the relationship between age at surgery and evolution of open bite. Complications were minimal and satisfactory outcomes were observed with a decrease in anterior open bite.

Conclusions: In this study we have observed that surgical treatment in patients with BWS and open bite accompanied by macroglossia seems to provide positive results with a satisfactory outcome in dentoskeletal alterations.

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Conflict of interest statement

Conflict of interest statement: The authors declare that there is no conflict of interests.

Figures

Figure 1
Figure 1
Intraoperative image. Surgical tongue reduction design.
Figure 2
Figure 2
One patient from group B. This patient has been operated on 3 times. Open bite and interdental spaces before starting orthodontic treatment.
Figure 3
Figure 3
One patient from group B. This patient has been operated on 4 times. He has achieved normocclusion after orthopaedic- orthodontic treatment.
See this image and copyright information in PMC

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