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Case Reports
. 2018;27(3):293-296.
doi: 10.1159/000488352. Epub 2018 Mar 13.

Sanjad-Sakati Syndrome: Oral Health Care

Yazan Hassona  1   2 , Lamis Rajab  3   2 , Dina Taimeh  1   2 , Crispian Scully  4
Affiliations
Case Reports

Sanjad-Sakati Syndrome: Oral Health Care

Yazan Hassona et al. Med Princ Pract. 2018.

Abstract

Objectives: The aim of this report is to describe the orofacial manifestations and dental management of a girl with Sanjad-Sakati syndrome.

Clinical presentation and intervention: The facial features included microcephaly, thin lips, beaked nose, low set ears, and a retrognathic mandible. An oral examination revealed oligodontia/hypodontia, small dental arches, a high arched palate, and a deep overbite and increased overjet. Oral rehabilitation involved full coverage prosthetic crowns on the upper central incisors, stainless steel crowns on the lower molars, and removable partial prostheses to replace missing teeth.

Conclusion: Recognition of orofacial features might help in the diagnosis of Sanjad-Sakati syndrome. Dental management of affected patients might be complicated by intellectual, neurological, and endocrine abnormalities.

Keywords: Dental health care; Hypoparathyroidism; Learning disability; Mental retardation; Sanjad-Sakati syndrome; Seizure disorder.

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Figures

Fig. 1
Fig. 1
Small hands with short and thin digits.
Fig. 2
Fig. 2
Oral findings included small dental arches, increased over bite, plaque-induced gingivitis, and multiple carious and missing teeth.
Fig. 3
Fig. 3
Small and pointed tongue.
Fig. 4
Fig. 4
Orthopantomography showing multiple missing teeth, delayed dental development, taurodontism, and incomplete rot formation of the lower first molars.
Fig. 5
Fig. 5
Oral rehabilitation using stainless steel crowns, prosthetic crowns, and a removable partial denture.
Fig. 6
Fig. 6
Erythematous candidiasis (denture stomatitis).
See this image and copyright information in PMC

References

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Publication types

Supplementary concepts