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Review
. 2018 Jun:27:2-5.
doi: 10.1016/j.prrv.2018.03.001. Epub 2018 Mar 15.

Cystic fibrosis papers of the year 2017

Affiliations
Review

Cystic fibrosis papers of the year 2017

Iolo Doull. Paediatr Respir Rev. 2018 Jun.

Abstract

The number of published articles on Cystic Fibrosis (CF) continues to increase year on year. The evidence base for small molecule therapies in CF has continued to expand, with evidence for lumacaftor/ivacaftor in younger patients and longer-term evidence in adults, and pivotal studies on tezacaftor/ivacaftor. There were reports on emerging CFTR mutation agnostic therapies, and new evidence for long standing therapies.

Keywords: Cystic fibrosis; Doxycycline; Ivacaftor; Lumacaftor; MRSA; Tezacaftor.

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