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Case Reports
. 2018 Apr 5:9:73.
doi: 10.4103/sni.sni_47_18. eCollection 2018.

Dorsal hemangioblastoma manifesting as holocord syringomyelia

Gautam Dutta  1 , Daljit Singh  1 , Hukum Singh  1 , Arvind K Srivastava  1 , Anita Jagetia  1 , Atul Agrawal  1
Affiliations
Case Reports

Dorsal hemangioblastoma manifesting as holocord syringomyelia

Gautam Dutta et al. Surg Neurol Int. .

Abstract

Background: Intramedullary spinal hemangioblastomas are known to be accompanied by syringomyelia.

Case description: Here, we report a patient who presented with symptoms of a Chiari malformation but was found to have a D4 intramedullary hemangioblastoma with a holocord syrinx.

Conclusions: Although rare, neurosurgeons should keep in mind the possibility of an intramedullary hemangioblastoma in patients presenting with symptoms of a Chiari malformation.

Keywords: Chiari malformation; differential diagnosis; hemangioblastoma; holocord; intramedullary; spinal; syringomyelia.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
MRI cervico-dorsal region showing a well-defined intramedullary lesion at D4 with syrinx rostral to the lesion
Figure 2
Figure 2
MRI whole spine showing associated holocord syrinx
See this image and copyright information in PMC

References

    1. Kumar J, Kumar A, Gupta S Neurological pictures. Chiari I malformation with holocord syrinx. J Neurol Neurosurg Psychiatry. 2007;78:146. - PMC - PubMed
    1. Pai SB, Krishna KN. Secondary holocord syringomyelia with spinal hemangioblastoma: A report of two cases. Neurol India. 2003;51:67–8. - PubMed
    1. Wu TC, Guo WY, Lirng JF, Wong TT, Chang FC, Luo CB, et al. Spinal cord hemangioblastoma with extensive syringomyelia. J Chin Med Assoc. 2005;68:40–4. - PubMed

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