Paediatric VIPoma: A Jamboree of Electrolytes
- PMID: 29744252
- PMCID: PMC5937463
- DOI: 10.5152/TJAR.2017.22220
Paediatric VIPoma: A Jamboree of Electrolytes
Abstract
Vasoactive intestinal peptide secreting tumour (VIPoma) is a rare type of neuroendocrine tumour (NET), primarily located in the tail of pancreas. This type of tumour presents with myriad of metabolic and electrolyte misbalances in the preoperative period, mainly due to increased vasoactive intestinal peptide (VIP) levels. Perioperative management of patients with VIPoma is challenging, especially when dealing with paediatric patients. The anaesthetic management of a two-year-old girl who was selected for VIPoma resection is hereby presented.
Keywords: Diarrhoea; dyselectrolytemia; hypokalaemia.
Conflict of interest statement
Conflict of Interest: No conflict of interest was declared by the authors.
Figures
References
-
- Verner JV, Morrison AB. Islet cell tumor and a syndrome of refractory watery diarrhea and hypokalemia. Am J Med. 1958;25:374–80. https://doi.org/10.1016/0002-9343(58)90075-5. - DOI - PubMed
-
- Anderson CW, Bennett JJ. Clinical Presentation and Diagnosis of Pancreatic Neuroendocrine Tumors. Surg Oncol Clin N Am. 2016;25:363–74. https://doi.org/10.1016/j.soc.2015.12.003. - DOI - PubMed
-
- Krejs GJ. VIPoma syndrome. Am J Med. 1987;82:37–48. https://doi.org/10.1016/0002-9343(87)90425-6. - DOI - PubMed
-
- Cavalli T, Giudici F, Santi R, Nesi G, Brandi ML, Tonelli F. Ventricular fibrillation resulting from electrolyte imbalance reveals vipoma in MEN1 syndrome. Fam Cancer. 2016;15:645–9. https://doi.org/10.1007/s10689-016-9906-4. - DOI - PubMed
-
- Dimitriadis GK, Weickert MO, Randeva HS, Kaltsas G, Grossman A. Medical management of secretory syndromes related to gastroenteropancreatic neuroendocrine tumours. Endocr Relat Cancer. 2016;23:R423–36. https://doi.org/10.1530/ERC-16-0200. - DOI - PubMed
Publication types
LinkOut - more resources
Full Text Sources
Other Literature Sources