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. 2017 Dec;5(4):251-258.
doi: 10.1007/s40136-017-0163-3. Epub 2017 Sep 30.

Diagnosis and Treatment of Congenital Sensorineural Hearing Loss

Divya A Chari  1 , Dylan K Chan  1
Affiliations

Diagnosis and Treatment of Congenital Sensorineural Hearing Loss

Divya A Chari et al. Curr Otorhinolaryngol Rep. 2017 Dec.

Abstract

Purpose of review: The aim of this report is to review current literature regarding the work-up and management of congenital sensorineural hearing loss.

Recent findings: Diagnostic evaluation of a newborn with sensorineural hearing loss begins with a complete audiologic evaluation and comprehensive history and physical exam. This review presents a diagnostic algorithm for the work-up of congenital hearing loss, focusing on the three following modalities: cytomegalovirus testing, genetic evaluation, and imaging.

Summary: Newborn hearing loss is a common problem and may be attributed to genetic and non-genetic factors. Complete diagnostic evaluation and treatment are essential for preventing delays in language development. Treatment consists of early intervention services and consideration of hearing aid amplification and cochlear implantation.

Keywords: Congenital hearing loss; cochlear implantation; cytomegalovirus; diagnosis; newborn hearing screen; prelingual deafness.

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Conflict of interest statement

Conflict of Interest: None. Conflict of Interest Dr. Chan and Dr. Chari have nothing to declare.

Figures

Fig. 1
Fig. 1
Basic diagnostic algorithm for congenital hearing loss
See this image and copyright information in PMC

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