Case Reports
doi: 10.1002/1097-0142(19850401)55:7<1446::aid-cncr2820550704>3.0.co;2-5.
Nephroblastomatosis and Wilms' tumor. Clinical experience and management of seven patients
- PMID: 2983856
- DOI: 10.1002/1097-0142(19850401)55:7<1446::aid-cncr2820550704>3.0.co;2-5
Item in Clipboard
Case Reports
Nephroblastomatosis and Wilms' tumor. Clinical experience and management of seven patients
Cancer.
.
Abstract
Nephroblastomatosis is an uncommon abnormality believed to represent the persistence of embryonal renal tissue. Its association with simultaneous or eventual Wilms' tumor has led to the speculation that it is a premalignant lesion. The accumulated clinical experience with this process and its progression to Wilms' tumor in three of seven individuals is discussed. It is concluded that conservative tissue sparing surgery, chemotherapy, and ultrasonographic follow-up are the approaches most appropriate for the management of these difficult patients.
Similar articles
-
Persistent renal blastema (nephroblastomatosis) as a frequent precursor of Wilms' tumor; a pathological and clinical review. Part 2. Significance of nephroblastomatosis in the genesis of Wilms' tumor.Am J Pediatr Hematol Oncol. 1980 Fall;2(3):253-61. Am J Pediatr Hematol Oncol. 1980. PMID: 6254388
-
Bilateral Wilms' tumors: a single-center experience with 19 cases.J Pediatr Surg. 2005 Aug;40(8):1289-94. doi: 10.1016/j.jpedsurg.2005.05.013. J Pediatr Surg. 2005. PMID: 16080934
-
The nephroblastomatosis complex and its relationship to Wilms' tumor: a clinicopathologic treatise.Perspect Pediatr Pathol. 1976;3:185-223. Perspect Pediatr Pathol. 1976. PMID: 184429
-
[Association of infantile nephroblastomatosis and Wilms' tumor: discussion of a clinical case and therapeutic problems, analysis of the literature].Pediatr Med Chir. 1994 Jan-Feb;16(1):95-9. Pediatr Med Chir. 1994. PMID: 8029102 Review. Italian.
-
Management of bilateral Wilms tumours.Pediatr Surg Int. 2017 Apr;33(4):461-469. doi: 10.1007/s00383-016-4047-2. Epub 2017 Jan 4. Pediatr Surg Int. 2017. PMID: 28054101 Review.
Cited by
-
An analysis of histology and DNA-ploidy in primary wilms tumors and their metastases and a study of the morphological effects of therapy.Virchows Arch A Pathol Anat Histopathol. 1987;410(6):487-94. doi: 10.1007/BF00781683. Virchows Arch A Pathol Anat Histopathol. 1987. PMID: 3031875
-
Perlman and Wiedemann-Beckwith syndromes: two distinct conditions associated with Wilms' tumour.Eur J Pediatr. 1992 Dec;151(12):895-8. doi: 10.1007/BF01954125. Eur J Pediatr. 1992. PMID: 1361910
-
Blastemal cells of nephroblastomatosis complex share an onco-developmental antigen with embryonic kidney and Wilms' tumor. An immunohistochemical study on polysialic acid distribution.Am J Pathol. 1988 Dec;133(3):596-608. Am J Pathol. 1988. PMID: 2849302 Free PMC article.
-
Nephroblastomatosis: the whole spectrum of abnormalities in one case.Pediatr Radiol. 1992;22(8):598-9. doi: 10.1007/BF02015362. Pediatr Radiol. 1992. PMID: 1337203
Publication types
MeSH terms
Substances
LinkOut - more resources
Medical